Citation

Zulkifli MFB, Aini NRB, Hashim SSM (2019) The Ex Utero Intrapartum Treatment (EXIT) Procedure in Huge Congenital Cervical Lymphatic Malformation. J Otolaryngol Rhinol 5:052. doi.org/10.23937/2572-4193.1510052

Copyright

© 2019 Zulkifli MFB, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.

CASE REPORT | OPEN ACCESSDOI: 10.23937/2572-4193.1510052

The Ex Utero Intrapartum Treatment (EXIT) Procedure in Huge Congenital Cervical Lymphatic Malformation

Muhd Faiz Bin Zulkifli1,2* Nor Rahimah Binti Aini2,3 and Siti Sabzah Mohd Hashim2

1Department of Otorhinolaryngology- Head and Neck Surgery, KPJ Healthcare University College, Malaysia

2Department of Pediatric Otorhinolaryngology- Head and Neck Surgery, Hospital Sultanah Bahiyah, Alor Setar, Kedah, Malaysia

3Department of Otorhinolaryngology- Head and Neck Surgery, Hospital University Sains Malaysia, Malaysia

Abstract

Abstract

Congenital giant cervical lymphatic malformation are rare tumors. Recent advances in prenatal diagnosis and delivery by ex utero intrapartum treatment (EXIT) have improved prenatal outcome.

Case

An otherwise healthy 35-year-old woman, gravida 5, para 4, was referred to our institution at 25 weeks' gestation with a diagnosis large neck mass in the fetus. Prenatal ultrasound and magnetic resonance imaging (MRI) findings suggested airway obstruction in the fetus. The EXIT procedure attempt to deliver the baby was successful.

Conclusion

Despite prenatal detection and diagnosis of airway compromise in a fetus with a huge cervical lymphatic malformation, securing the fetal airway can be challenging. Large mass can completely distort normal tissue and anatomy.