Congenital giant cervical lymphatic malformation are rare tumors. Recent advances in prenatal diagnosis and delivery by ex utero intrapartum treatment (EXIT) have improved prenatal outcome.
An otherwise healthy 35-year-old woman, gravida 5, para 4, was referred to our institution at 25 weeks' gestation with a diagnosis large neck mass in the fetus. Prenatal ultrasound and magnetic resonance imaging (MRI) findings suggested airway obstruction in the fetus. The EXIT procedure attempt to deliver the baby was successful.
Despite prenatal detection and diagnosis of airway compromise in a fetus with a huge cervical lymphatic malformation, securing the fetal airway can be challenging. Large mass can completely distort normal tissue and anatomy.