The double lip is a rare and benign developmental alteration characterized by increased lip tissue, specially of the upper lip. Its etiology is linked to congenital factors, such as Ascher Syndrome, or being acquired by labial trauma. The main related complaint is the aesthetic, and the diagnosis is predominantly based on the clinical aspect. The hormonal exams are part of the differential diagnosis. Regarding the treatment, there are several techniques of surgical excision but the elliptical incision, also known as wedge, has presented better results and low rate of postoperative sequelae. The objective of this study is to report a bilateral double-lip clinical case, correlating it with what is current in the literature. Patient M.J.S.S., female, leukoderma, 55-years-old, attended the Center for Dental Specialties (CDS) of ASCES-UNITA due to the presence of an upper lip lesion; the patient reported aesthetic complaint and during the physical examination a bilateral alteration in the upper lip was observed, which was expressed when she smiled with double-lip characteristics, in addition to dental absence of all anterior and superior dental elements. After the diagnostic hypothesis, the surgical treatment chosen was total excision of the excess tissue with incision in ellipse and referral of the specimen for histopathological examination. After 7 days the synthesis material was removed with signs of good healing. Patient had follow-up for 3 months without signs of relapse. It is concluded that the double lip is rare affection lesion, which practically has a clinical diagnosis, and shows several forms of surgical treatment that should only be performed through aesthetic and/or functional complaint of the patient. Correct diagnosis is essential for the elimination of Ascher syndrome, thus leading to the best possible treatment.