Table 1: List of clinical and molecular markers meausre collected from the patient cohort.

Summary of abbreviated data terms

Clinical measure

Notation

Delta at 3, 6, 12 months

Predicted forced vital capacity (FVC%)

dp_d1

dp_3, dp_6, dp_12

Predicted forced expiratory volume (FEV1%)

d1p_d1

d1p_3, d1p_6, d1p_12

Diffusing capacity of the lung for carbon dioxide (DLCO%)

DLCO

DLCO_3, DLCO_6, DLCO_12

Gender, age, lung physiology index (GAP)

GAP

 

Body mass index (BMI)

BMI_d1

BMI_3, BMI_6, BMI_12

Six minute walk test (6MW)

w6MW_d1

wp_3, wp_6, wp_12

Mitochondrial DNA/genomic DNA ratio (Mt DCN)

Y1