| Reference | Age/Sex | FHx | BP | SC | Imaging findings | Opposite kidney /other organs | Follow up |
| Hazarika et al. 2014 [8] | 49/ Male | Negative | NL | NL | CT Diffusely involved with cysts and residual normal renal parenchyma. No enhancing soft tissue component or bands. Normal collecting system. | Not involved | Not mentioned |
| Miyamoto et al. 2010 | 52/ Male | Negative | NL | NL | CT Multiple large cysts scattered diffusely. | Not involved | Follow up |
| Curry N S et al. 1993 [10] | 57/ Male | Negative | NA | NL | CT A near complete replacement of affected kidney by cysts of varying sizes and calyceal distortion. | 2 small, simple cysts in upper pole | CT follow up for 30 years |
| Bae E H et al. 2013 [9] | 51/ Male | Negative | NA | NL | CT
Revealed enlarged kidney with variable-sized round, well marginated multiple cysts without capsule formation or solid content.
MRI Six months, later showed numerous cysts in the right kidney with no changes according to previous CT |
Not involved | Follow up by MRI in 6 months |
| Park B S et al. 2007 [1] | 31/ Female | Negative | NL | NL | CT
Enlarged kidney filled with variable sized multiple cysts with enhancing normal renal tissues between the cysts.
MRI Enlarged kidney with multiple cysts of varying size without capsule formation. There were no solid portions within the cysts and normally enhancing renal parenchyma seen between the cysts. |
Not involved | Laparoscopic Radical nephrectomy |
| Hwang D Y et al. 1999 [2] | 31/ Male | Negative | NL | NL | CT Enlarged kidney, variable size well marginated multiple cysts with no capsule formation. Cysts separate by normal parenchymal bands. | 2 simple, cortical cysts. Other organs normal | Follow up with creatinine for 18 months |
| 44/ Male | Negative | High | NL | Enlarged kidney with variable size multiple cysts separate by enhancing septae | Not involved | Follow up 15 months with Creatinine | |
| Farinha A et al. 2011 [8] | 26/ Female | Negative | High | NL | CT Diffusely enlarged kidney containing multiple cysts of varying sizes. | Not involved | Follow up radiologically for 10 years |
| Zafar Neyaz et al. 2012 [4] | 16/ Male | Negative | NL | NL | USS
Multiple small, simple cysts with relative sparing of the upper pole parenchyma.
MRI Multiple simple cysts mainly involving middle and inferior polar region of the right kidney without any solid component or thick septae. |
Not involved | Follow up annually with USS & creatinine |
| Solack et al. 2013 [6] | 16/ Male | Negative | High | NL | USS
Multiple variable sized cysts in the upper pole of the kidney
CT The upper pole of the right kidney was filled with multiple cysts of different sizes with enhancing normal renal tissue between the cysts. MRI Upper pole cysts without capsule formation. There were no solid areas within and renal parenchyma between the cysts was normally enhancing DMSA Decreased renal uptake at the upper half of the right kidney |
Not involved | Right upper pole hemi nephrectomy
to control BP
2 year follow up with USS and creatinine |