Relevant aspects

• Associations very infrequent, but situations do exist. Need for more knowledge.

• Associations of complex etiopathogenesis. Not fully clarified.

• Lack of specific diagnostic and therapeutic protocols.

• Search for tumours of various kinds, synchronous and metachronous.

• Functional situations (catecholamine secretion) and malignancy situations.

Diagnostic and therapeutic strategy (some aspects)

• Individualise therapeutic priorities: functional tumours?

• Interdisciplinary collaboration.

• Follow-up throughout life (metachronous tumours).

• Variable prognosis. There are situations of malignancy.