Table 1: Etiologies and mortality of each subgroup of patients with Hemophagocytic Syndrome.

Etiologies

n = 30

Mortality during the admission+

Mortality after discharge++

Autoimmune diseases

n = 10

n = 1

n = 0

Systemic Lupus Erythematosus (SLE)

5

1

0

Adult Still's Disease (ASD)

3

0

0

Rheumatoid arthritis

1

0

0

IgG4 Sclerosing Disease

1

0

0

Hematological Malignancies Diseases

n = 12

n = 8*

n = 3

Non-Hodgkin's Lymphoma

3

1

1

Myelodysplastic síndrome

3

2

1

Acute leukemia

3

3

-

Lymphoma extranodal NK cell

1

1

-

Multiple Myeloma

1

0

1

Probably lymphoproliferative disease

1

1

-

Infectious diseases

n = 2

n = 1

n = 0

Pneumocystis jirovencii in a patient with HIV

1

1

0

Gastroenteritis by Campylobacter jejuni

1

0

0

Malignant Solid tumor disease

n = 1

n = 0

n = 1

Glioblastoma multiforme (GM) with temozolomide

1

0

1

HPS without defined etiology

n = 5

3

n = 0

HIV: Human Immunodeficiency Virus.
NK: Natural Killer.
+Mortality secondary to HPS.
++Mortality secondary to primary etiology.
*p = 0.029.