Table 1: Abdominal neoplasms of neurofibromatosis.
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Neurogenic Tumors Neurofibromas Plexiform Neurofibromas Malignant Peripheral Nerve Sheath Tumor Ganglineuroma |
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Neuroendocrine Tumour Carcinoid Tumor Pheochromocytoma Paraganglioma Periampullary neuroendocrine tumors (Insulinoma, Glucagonoma, Somatostatinoma) |
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Non-Neurogenic Tumors GIST |
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Embryonal Tumors Neuroblastoma Wilms Tumor Rhabdomyosarcoma |
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Other Tumors Adenocarcinomas Extra-abdominal tumors (leukemia, lymphomas) |