Table 1: Abdominal neoplasms of neurofibromatosis.
Neurogenic Tumors Neurofibromas Plexiform Neurofibromas Malignant Peripheral Nerve Sheath Tumor Ganglineuroma |
Neuroendocrine Tumour Carcinoid Tumor Pheochromocytoma Paraganglioma Periampullary neuroendocrine tumors (Insulinoma, Glucagonoma, Somatostatinoma) |
Non-Neurogenic Tumors GIST |
Embryonal Tumors Neuroblastoma Wilms Tumor Rhabdomyosarcoma |
Other Tumors Adenocarcinomas Extra-abdominal tumors (leukemia, lymphomas) |